More

Featuring fresh takes and real-time analysis from HuffPost's signature lineup of contributors
Harold Pollack

GET UPDATES FROM Harold Pollack
 

Should We Screen Newborns for Fragile X Syndrome?

Posted: 10/13/10 01:29 AM ET

My latest long-form article, in the November issue of American Prospect, concerns the dilemmas of newborn genetic screening, focusing on a condition called fragile X syndrome.

Fragile X is the most common heritable form of intellectual disability. Many individuals with fragile X syndrome are also diagnosed with autism and related symptoms. Especially if you've never heard of fragile X. I really hope that you read this piece.

Fragile X is reasonably complicated. And these complications really matter for both clinical interventions and for public policy. Fragile X therefore exemplifies broader dilemmas we will increasingly confront within our health care system.

As in the case of sickle cell, supposed "carriers" face characteristic health concerns. People with the same genetic markers display very different impairments and symptoms -- including no apparent symptoms at all. Partly because of this variation, fragile X is often overlooked or misdiagnosed.

Many parents spend years chasing down false leads before proper diagnosis is made. They also have other children before proper diagnosis is made. Many people with fragile X-related conditions are diagnosed through the diagnosis of a younger sibling. Newborn screening might prevent this "diagnostic odyssey," but aggressive screening brings other problems and economic challenges, too.

Fragile X highlights the embarrassing mismatch between our medical care system's aspirations of personalized genomic medicine and that system's limited everyday capacities to actually use such information well.

We continue to pump money into research and advanced treatments for conditions influenced by detectable genetic traits. That's good, but we don't support the everyday patient and provider experiences of genetic screening and care with equal vigor. Because of this imbalance, advances in genetic science continually raise questions that our medical care system is ill-equipped to address. We need to do better.

 

Follow Harold Pollack on Twitter: www.twitter.com/@haroldpollack

 
 
  • Comments
  • 8
  • Pending Comments
  • 0
  • View FAQ
Comments are closed for this entry
View All
Favorites
Recency  | 
Popularity
06:58 PM on 10/24/2010
I think the kind of education that needs to be promoted is not one that can be supported under the limited science of the current medical paradigm which offers a Newtonian man as machine approach and is geared in all facets to a Darwinistic approach of survival of the fittest. Cutting edge biology and epigenetics demonstrates that our current medical paradigm (which is the root of how all treatments and education plans are implemented) is completely outmoded and faulty.
Education yes! But where will awareness get us in a medical paradigm that cannot offer solutions?
What has genetic testing really offered in regards to potential of human development?
Is it the name of the disease that dictates the potential of the individual who happens to be named or labeled by it?
Yes, it is sad, and plans are needed. But I personally think the bandaid symptomatic approach being followed by a medical system that has not caught up and implemented a quantum view is one of the biggest parts of the problem. When awareness is achieved, the solutions are looked for down the wrong road.
We are all connected and we all need to understand those who face more challenges than average, because they are the challenges of all of us. TO not face them together and not support of fellow brothers and sisters in need leads us down road of destruction for humanity.
HUFFPOST SUPER USER
momstudent
09:58 AM on 10/18/2010
Six comments (two by me) from an article which millions of parents and future parents need to be educated about. Is it fear? I don't know. Very sad indeed. I work with these children and families every day and they are not going away, and at some point will need a transition plan, circle of support etc..very sad indeed.
11:03 AM on 10/16/2010
Our son Tim has FXS and I have experienced and seen many others go through the painful odyssey of seeking a correct diagnosis. Pediatricians are now more diligent in screening babies/toddlers for autism and this is helping some families to get an earlier diagnosis for FXS since many of the symptoms such as language delay and sensory integration problems are also seen in FXS. Early intervention can really help the child and the family. Our first 2.5 years before diagnosis were a nightmare of no sleep, feeding problems, doctor visits, hospitalizations and CRYING(both Tim and myself). Let's focus research on identifying early signs and educating pediatricians on FXS, Williams Syndrome, Prader-Willi, Tuberous Sclerosis and just plain developmental delays which could be helped with early intervention and result in better long term overall quality of life. Tim is now 19 and is the kindest, nicest, happiest person I have ever known and we should not as a society marginalize and exterminate those with certain genetic conditions just because it may be costly to provide them with care. I would promote more first/second year screening of infants for FXS who are presenting with some concerns to either their parents or physicians.
HUFFPOST SUPER USER
momstudent
12:00 PM on 10/16/2010
Your son is fortunate his parents kept trying and demanding answers. All of the genetic syndromes you spoke of are needed to be screened more often. However, the public will be stunned when they finally accept the number one preventable disability with children is Fetal Alcohol Exposure and Drug Exposure. At work, clinics are ran for Williams Syndrome education for families at least twice a year, and FAS every month. Sadly, either adoptive or grand parents are told their children have been exposed. I have seen the face of a 15 year boy be told his bio-mother abused alcohol and or drugs while pregnant, and this is the reason his handwriting is poor, his attention is short, as well as his temper and why he continues to make poor choices. There are only two certainties in this world, one we do not get to pick or choose our parents or siblings, two as parents, we do not get to pick or choose our children, even if they are adopted. They come to us how they are, all of the great qualities we would never change, and all of the challenges we would.
HUFFPOST SUPER USER
momstudent
12:00 PM on 10/15/2010
Agreed 100%. Through my job and advocate work there are far more children with Fragile X Syndrome than we want to admit. I witnessed one family discover rather late, all three of their boys have Fragile X with different levels of functioning. The symptoms are very similar to Autism and sadly, parents do not follow up on the medical component of diagnostics and begin expensive and not replicated interventions.
photo
HUFFPOST SUPER USER
sistersuperior
union made
11:02 PM on 10/14/2010
Can screening for this be done in utero? If so, how early in the pregnancy?
10:16 AM on 10/13/2010
Luckily, or, thanks be to 0bama, under the new Healthcare Reform Act, insurers won't be able to reduce or deny coverage for pre-existing conditions.
photo
HUFFPOST SUPER USER
Codefile
Does anybody know the tab to that song?
01:02 AM on 10/13/2010
Should we screen newborns? The answer is yes.
All options are available with choice. Big brother
needs to know if you have A N Y pre-existing "conditions"
and society is protected this way. From us.